Hirayama disease; an atypical clinical manifestation of a cervical myelopathy with typical MRI features

Hirayama disease; an atypical clinical manifestation of a cervical myelopathy with typical MRI features.

To cite: Salome M, Barkhof F, Visser L. BMJ Case Rep Published online: [please include Day Month Year] doi:10.1136/bcr-2016217780 DESCRIPTION A young man was evaluated because of progressive weakness in both hands since 2 years. He played sport on a high level and experienced difficulties in catching the ball. Flexion of the neck caused paresthesias and an electric shock like sensation in both ...

Dynamic myelopathy in Hirayama disease.

http://dx.doi.org/10.1016/j.spinee.2014.06.026 1529-9430/ 2014 Elsevier Inc. All rights reserved. months despite physiotherapy. There was no history of cold paresis. Neurologic examination revealed atrophy in all muscles of the forearm and intrinsic hand muscles, no fasciculations, right upper limb (UL) hypotonia, distal and extensor predominant motor deficit, right UL pathologic hyperreflexia,...

Recurrent cervical carcinoma: Typical and atypical MRI and CT findings

Correlations of clinical, neuroimaging, and electrophysiological features in Hirayama disease

Hirayama disease (HD) is characterized by development of asymmetric forearm muscle atrophy during adolescence with or without focal cervical spinal cord atrophy. The purpose of this study is to assess the correlation of clinical symptoms, disease progression, and electrophysiological findings with cervical spine magnetic resonance imaging (MRI) findings.The medical records, cervical spine MRIs,...

Hirayama Disease: A Rare Disease with Unusual Features

Hirayama disease, also known as monomelic amyotrophy (MMA), is a rare cervical myelopathy that manifests itself as a self-limited, asymmetrical, slowly progressive atrophic weakness of the forearms and hands predominantly in young males. The forward displacement of the posterior dura of the lower cervical dural canal during neck flexion has been postulated to lead to lower cervical cord atrophy...